GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Progressive sclerosing poliodystrophy

An  Autosomal recessive  mode(s) within the Neurodegenerative disorders  category

Likely pathogenic 1
Pathogenic/Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_002693.3(POLG):c.368T>G (p.Val123Gly) Single nucleotide variant Chr15:89333387 Likely pathogenic Missense variant rs2509275684 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_002693.3(POLG):c.911T>G (p.Leu304Arg) Single nucleotide variant Chr15:89329055 Pathogenic/Likely pathogenic Missense variant rs121918044 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution