GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Multiple endocrine neoplasia, type 1

An  Autosomal dominant  mode(s) within the Cancer disorders  category

Benign 1
Benign/Likely benign 2
Conflicting classifications of pathogenicity 2
Likely pathogenic 3
Pathogenic 3
Pathogenic/Likely pathogenic 2
Uncertain significance 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000051.4(ATM):c.7381C>A (p.Arg2461Ser) Single nucleotide variant Chr11:108330287 Uncertain significance Missense variant|intron variant rs201314561 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_024529.5(CDC73):c.70G>T (p.Glu24Ter) Single nucleotide variant Chr1:193122270 Likely pathogenic Nonsense rs2527281270 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.428T>G (p.Leu143Arg) Single nucleotide variant Chr11:64809682 Likely pathogenic Missense variant|non-coding transcript variant rs2136178143 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.137A>T (p.His46Leu) Single nucleotide variant Chr11:64809973 Likely pathogenic Missense variant|non-coding transcript variant rs2136192730 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.784-129T>A Single nucleotide variant Chr11:64807348 Benign/Likely benign Intron variant rs536461697 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.725C>T (p.Ala242Val) Single nucleotide variant Chr11:64807610 Pathogenic/Likely pathogenic Missense variant rs2136141530 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.818T>C (p.Leu273Pro) Single nucleotide variant Chr11:64807185 Conflicting classifications of pathogenicity Missense variant rs1592647281 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.913-42G>C Single nucleotide variant Chr11:64806410 Benign Intron variant rs529037188 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.1212C>G (p.Leu404=) Single nucleotide variant Chr11:64805172 Benign/Likely benign Synonymous variant rs577268289 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.446-2A>C Single nucleotide variant Chr11:64808101 Pathogenic Splice acceptor variant rs886042035 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.1174del (p.Glu392fs) Deletion Chr11:64805646 Pathogenic/Likely pathogenic Frameshift variant rs386134247 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.758C>T (p.Ser253Leu) Single nucleotide variant Chr11:64807577 Conflicting classifications of pathogenicity Missense variant rs386134259 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.548G>A (p.Trp183Ter) Single nucleotide variant Chr11:64807997 Pathogenic Nonsense rs794728650 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)
NM_001370259.2(MEN1):c.1252G>A (p.Asp418Asn) Single nucleotide variant Chr11:64805132 Pathogenic Missense variant rs104894264
NM_000455.5(STK11):c.749C>T (p.Thr250Met) Single nucleotide variant Chr19:1221227 Uncertain significance Missense variant rs876661238 .Laboratory of Molecular and Cytogenetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS)

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution