GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

Methylmalonic aciduria, cblB type

An  Autosomal recessive  mode(s) within the Metabolic disorders  category

Likely pathogenic 3
Pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_052845.4(MMAB):c.571C>G (p.Arg191Gly) Single nucleotide variant Chr12:109561053 Likely pathogenic Missense variant|non-coding transcript variant rs376128990 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_052845.4(MMAB):c.572G>C (p.Arg191Pro) Single nucleotide variant Chr12:109561052 Likely pathogenic Missense variant|non-coding transcript variant rs746219370 .Lifecell International Pvt. Ltd
NM_052845.4(MMAB):c.580A>G (p.Arg194Gly) Single nucleotide variant Chr12:109561044 Likely pathogenic Missense variant|non-coding transcript variant rs2136198139 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_052845.4(MMAB):c.197-1G>T Single nucleotide variant Chr12:109568864 Pathogenic Splice acceptor variant rs763935916 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar