GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Marfan syndrome

An  Autosomal dominant  mode(s) within the Cardiovascular disorders  category

Conflicting classifications of pathogenicity 3
Likely pathogenic 14
Pathogenic 5
Pathogenic/Likely pathogenic 4
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000138.5(FBN1):c.8552_8553del (p.Lys2851fs) Deletion Chr15:48411053 - 48411054 Likely pathogenic Frameshift variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.2956del (p.Ala986fs) Deletion Chr15:48489977 Likely pathogenic Frameshift variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.3464-1G>C Single nucleotide variant Chr15:48487201 Pathogenic Splice acceptor variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.3458G>T (p.Cys1153Phe) Single nucleotide variant Chr15:48487317 Pathogenic Missense variant rs140599 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_000138.5(FBN1):c.1637G>A (p.Cys546Tyr) Single nucleotide variant Chr15:48510121 Likely pathogenic Missense variant rs112644647 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.247+9A>G Single nucleotide variant Chr15:48613001 Conflicting classifications of pathogenicity Intron variant rs1298547542 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_000138.5(FBN1):c.7817T>A (p.Val2606Asp) Single nucleotide variant Chr15:48420689 Likely pathogenic Missense variant rs2141220600 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5993G>T (p.Cys1998Phe) Single nucleotide variant Chr15:48444585 Likely pathogenic Missense variant rs1085307531 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5966G>C (p.Cys1989Ser) Single nucleotide variant Chr15:48444612 Likely pathogenic Missense variant rs1597531796 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5671G>A (p.Asp1891Asn) Single nucleotide variant Chr15:48448768 Pathogenic/Likely pathogenic Missense variant rs193922216 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5621G>T (p.Cys1874Phe) Single nucleotide variant Chr15:48448818 Likely pathogenic Missense variant rs2141252159 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.4491C>G (p.Cys1497Trp) Single nucleotide variant Chr15:48468503 Likely pathogenic Missense variant rs2043341481 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.3635G>A (p.Cys1212Tyr) Single nucleotide variant Chr15:48485451 Likely pathogenic Missense variant rs1057522908 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.3766A>G (p.Asn1256Asp) Single nucleotide variant Chr15:48483890 Conflicting classifications of pathogenicity Missense variant rs772890884 .Molecular Lab, Department of Haematology, Christian Medical College
NM_000138.5(FBN1):c.5917+1G>T Single nucleotide variant Chr15:48445375 Pathogenic/Likely pathogenic Splice donor variant rs363808 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.6113G>C (p.Cys2038Ser) Single nucleotide variant Chr15:48441771 Likely pathogenic Missense variant rs363804 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000138.5(FBN1):c.6698C>T (p.Pro2233Leu) Single nucleotide variant Chr15:48432907 Likely pathogenic Missense variant rs1566894783 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.6236C>G (p.Ser2079Cys) Single nucleotide variant Chr15:48437845 Likely pathogenic Missense variant rs1555395263 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.1463G>A (p.Cys488Tyr) Single nucleotide variant Chr15:48515392 Pathogenic/Likely pathogenic Missense variant rs1555400372 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5917+6T>C Single nucleotide variant Chr15:48445370 Pathogenic/Likely pathogenic Intron variant rs1555395742 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.6004C>T (p.Pro2002Ser) Single nucleotide variant Chr15:48444574 Likely pathogenic Missense variant rs1057519320 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_000138.5(FBN1):c.7039_7040del (p.Met2347fs) Deletion Chr15:48427731 - 48427732 Pathogenic Frameshift variant rs794728319 .Lifecell International Pvt. Ltd
NM_000138.5(FBN1):c.1973G>A (p.Arg658Gln) Single nucleotide variant Chr15:48503927 Uncertain significance Missense variant rs794728181 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.5096A>G (p.Tyr1699Cys) Single nucleotide variant Chr15:48463210 Pathogenic Missense variant rs387906622 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000138.5(FBN1):c.3725G>A (p.Cys1242Tyr) Single nucleotide variant Chr15:48483931 Pathogenic Missense variant rs137854471 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001999.4(FBN2):c.2945G>T (p.Cys982Phe) Single nucleotide variant Chr5:128349391 Conflicting classifications of pathogenicity Missense variant rs1057519321 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_000138.5(FBN1):c.1130G>A (p.Cys377Tyr) Single nucleotide variant Chr15:48520676 Likely pathogenic Missense variant rs1597583989 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution