GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Li-Fraumeni syndrome

An  Autosomal dominant  mode(s) within the Cancer disorders  category

Likely pathogenic 1
Pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000546.6(TP53):c.861del (p.Asn288fs) Deletion Chr17:7673759 Pathogenic Frameshift variant|non-coding transcript variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000546.6(TP53):c.289G>A (p.Val97Ile) Single nucleotide variant Chr17:7676080 Uncertain significance Missense variant rs730882023
NM_000546.6(TP53):c.817C>T (p.Arg273Cys) Single nucleotide variant Chr17:7673803 Pathogenic/Likely pathogenic Missense variant rs121913343 .Biotechnology, Institute of Science, Nirma University
.Neuberg Centre For Genomic Medicine, NCGM
NM_000546.6(TP53):c.1031T>C (p.Leu344Pro) Single nucleotide variant Chr17:7670678 Likely pathogenic Missense variant|3 prime UTR variant rs121912662

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution