GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Kabuki syndrome

An  Autosomal dominant  mode(s) within the Neurodevelopmental disorders  category

Likely pathogenic 4
Pathogenic/Likely pathogenic 1
Uncertain significance 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001291415.2(KDM6A):c.3886C>T (p.Leu1296Phe) Single nucleotide variant ChrX:45089924 Uncertain significance Missense variant|non-coding transcript variant rs2523335532 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_003482.4(KMT2D):c.1258+5G>C Single nucleotide variant Chr12:49052559 Uncertain significance Intron variant .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_003482.4(KMT2D):c.3231dup (p.Val1078fs) Duplication Chr12:49050356 - 49050357 Likely pathogenic Frameshift variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_003482.4(KMT2D):c.7644del (p.Lys2548fs) Deletion Chr12:49040126 Likely pathogenic Frameshift variant rs2498395548 .Lifecell International Pvt. Ltd
NM_003482.4(KMT2D):c.15311G>T (p.Cys5104Phe) Single nucleotide variant Chr12:49026655 Likely pathogenic Missense variant rs2120361380 .Department Of Genetics, Lifeline Super Speciality Hospital, Adoor.
NM_003482.4(KMT2D):c.6109G>C (p.Asp2037His) Single nucleotide variant Chr12:49042089 Likely pathogenic Missense variant rs2120552716 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_003482.4(KMT2D):c.8059C>T (p.Arg2687Ter) Single nucleotide variant Chr12:49039605 Pathogenic/Likely pathogenic Nonsense rs1555191598 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
.Lifecell International Pvt. Ltd

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution