GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Joubert syndrome

An  Autosomal recessive, X-linked dominant  mode(s) within the Neurodevelopmental disorders  category

Conflicting classifications of pathogenicity 5
Likely pathogenic 3
Pathogenic 3
Pathogenic/Likely pathogenic 9
Uncertain significance 3

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001134831.2(AHI1):c.1799_1802del (p.Lys600fs) Microsatellite Chr6:135442692 - 135442695 Pathogenic/Likely pathogenic Frameshift variant rs1786504555 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Suma Genomics
NM_001134831.2(AHI1):c.1765C>T (p.Arg589Ter) Single nucleotide variant Chr6:135447022 Pathogenic Nonsense rs267606641 .Lifecell International Pvt. Ltd
NM_001174150.2(ARL13B):c.89A>G (p.Asp30Gly) Single nucleotide variant Chr3:93995903 Uncertain significance Missense variant|5 prime UTR variant|non-coding transcript variant|intron variant rs2471926773 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001352754.2(ARMC9):c.879G>A (p.Thr293=) Single nucleotide variant Chr2:231240041 Pathogenic/Likely pathogenic Synonymous variant|non-coding transcript variant|intron variant rs766572502 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_001378615.1(CC2D2A):c.4230G>T (p.Trp1410Cys) Single nucleotide variant Chr4:15589595 Likely pathogenic Missense variant rs2475127881 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001378615.1(CC2D2A):c.4088G>T (p.Gly1363Val) Single nucleotide variant Chr4:15587838 Conflicting classifications of pathogenicity Missense variant rs762683334 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001378615.1(CC2D2A):c.4555T>G (p.Trp1519Gly) Single nucleotide variant Chr4:15599587 Likely pathogenic Missense variant rs1577406415 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_025114.4(CEP290):c.4805C>T (p.Thr1602Met) Single nucleotide variant Chr12:88083854 Conflicting classifications of pathogenicity Missense variant rs369451049 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_025114.4(CEP290):c.5745dup (p.Lys1916Ter) Duplication Chr12:88071890 - 88071891 Pathogenic/Likely pathogenic Nonsense rs751361090 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_025114.4(CEP290):c.5668G>T (p.Gly1890Ter) Single nucleotide variant Chr12:88077263 Pathogenic/Likely pathogenic Nonsense rs137852832 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
.Suma Genomics
NM_001384732.1(CPLANE1):c.6114del (p.Asp2039fs) Deletion Chr5:37173812 Likely pathogenic Frameshift variant rs2547674026 .Lifecell International Pvt. Ltd
NM_001384732.1(CPLANE1):c.3056_3059dup (p.Trp1020fs) Microsatellite Chr5:37206286 - 37206287 Pathogenic/Likely pathogenic Frameshift variant rs769934551 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_001384732.1(CPLANE1):c.81G>A (p.Lys27=) Single nucleotide variant Chr5:37247618 Uncertain significance Synonymous variant rs1264949337 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_001382391.1(CSPP1):c.1698-1G>C Single nucleotide variant Chr8:67131950 Pathogenic Splice acceptor variant rs2129554176 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_173348.2(FAM149B1):c.2T>G (p.Met1Arg) Single nucleotide variant Chr10:73168341 Uncertain significance Missense variant|initiator_codon_variant rs569932117 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_019892.6(INPP5E):c.1303C>T (p.Arg435Trp) Single nucleotide variant Chr9:136432563 Pathogenic Missense variant rs756789619 .Manipal Hospitals, Manipal Hospital
NM_017777.4(MKS1):c.958G>A (p.Val320Ile) Single nucleotide variant Chr17:58210980 Conflicting classifications of pathogenicity Missense variant rs386834053 .Diagnostics Division, CENTRE FOR DNA FINGERPRINTING AND DIAGNOSTICS
NM_017777.4(MKS1):c.1450_1453dup (p.Thr485fs) Duplication Chr17:58206501 - 58206502 Pathogenic/Likely pathogenic Frameshift variant|intron variant rs386834044 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_016464.5(TMEM138):c.287A>G (p.His96Arg) Single nucleotide variant Chr11:61366203 Pathogenic/Likely pathogenic Missense variant|non-coding transcript variant rs387907132 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001173990.3(TMEM216):c.218G>A (p.Arg73His) Single nucleotide variant Chr11:61393965 Pathogenic/Likely pathogenic Missense variant rs201108965 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001077418.3(TMEM231):c.241C>T (p.Leu81Phe) Single nucleotide variant Chr16:75555872 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs376555896 .Lifecell International Pvt. Ltd
NM_153704.6(TMEM67):c.514C>T (p.Arg172Ter) Single nucleotide variant Chr8:93765413 Pathogenic/Likely pathogenic Nonsense|non-coding transcript variant rs765468645 .Institute of Medical Genetics and Genomics, Sir Ganga Ram Hospital
NM_153704.6(TMEM67):c.2086C>T (p.Leu696Phe) Single nucleotide variant Chr8:93797456 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs863225238 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution