GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Hyperimmunoglobulin D with periodic fever

An  Autosomal recessive  mode(s) within the Immune disorders  category

Likely pathogenic 1
Pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000431.4(MVK):c.1043T>C (p.Leu348Pro) Single nucleotide variant Chr12:109596429 Uncertain significance Missense variant|non-coding transcript variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000431.4(MVK):c.1097A>G (p.Asp366Gly) Single nucleotide variant Chr12:109596483 Likely pathogenic Missense variant|3 prime UTR variant|non-coding transcript variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000431.4(MVK):c.1162C>T (p.Arg388Ter) Single nucleotide variant Chr12:109596548 Pathogenic Nonsense rs104895360 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000431.4(MVK):c.1129G>A (p.Val377Ile) Single nucleotide variant Chr12:109596515 Pathogenic/Likely pathogenic Missense variant rs28934897 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution