GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Hereditary spherocytosis

An  Autosomal dominant, Autosomal recessive  mode(s) within the Blood disorders  category

Conflicting classifications of pathogenicity 4
Likely pathogenic 2
Pathogenic 1
Pathogenic/Likely pathogenic 3
Uncertain significance 4

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000037.4(ANK1):c.5633G>A (p.Gly1878Glu) Single nucleotide variant Chr8:41661476 Uncertain significance Missense variant|intron variant rs778450388 .Subrahamanyam Lab, Department of Biochemistry, National Institute of Nutrition, Indian Council of Medical Research
NM_000037.4(ANK1):c.4783G>A (p.Ala1595Thr) Single nucleotide variant Chr8:41672667 Uncertain significance Missense variant|intron variant rs1204538439 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_000037.4(ANK1):c.3325C>T (p.Gln1109Ter) Single nucleotide variant Chr8:41694594 Pathogenic/Likely pathogenic Nonsense rs2150593157 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000342.4(SLC4A1):c.2656C>A (p.Leu886Met) Single nucleotide variant Chr17:44250538 Conflicting classifications of pathogenicity Missense variant rs150340150 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000342.4(SLC4A1):c.2716G>C (p.Glu906Gln) Single nucleotide variant Chr17:44250478 Conflicting classifications of pathogenicity Missense variant rs199694087 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000342.4(SLC4A1):c.2573C>A (p.Ala858Asp) Single nucleotide variant Chr17:44251241 Pathogenic/Likely pathogenic Missense variant rs121912751 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
.Neuberg Centre For Genomic Medicine, NCGM
NM_000342.4(SLC4A1):c.1765C>T (p.Arg589Cys) Single nucleotide variant Chr17:44255708 Pathogenic/Likely pathogenic Missense variant rs121912745 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000342.4(SLC4A1):c.1766G>A (p.Arg589His) Single nucleotide variant Chr17:44255707 Pathogenic Missense variant rs121912744 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000342.3(SLC4A1):c.118G>A (p.Glu40Lys) Single nucleotide variant Chr17:44261625 Conflicting classifications of pathogenicity Missense variant rs45562031 .Bioinformatics dept., Datar Cancer Genetics Limited, India
NM_003126.4(SPTA1):c.1422G>T (p.Gln474His) Single nucleotide variant Chr1:158672125 Uncertain significance Missense variant rs762010257 .Subrahamanyam Lab, Department of Biochemistry, National Institute of Nutrition, Indian Council of Medical Research
NM_001355436.2(SPTB):c.1509G>C (p.Lys503Asn) Single nucleotide variant Chr14:64795472 Uncertain significance Missense variant rs751281187 .Neuberg Centre For Genomic Medicine, NCGM
.Subrahamanyam Lab, Department of Biochemistry, National Institute of Nutrition, Indian Council of Medical Research
NM_001355436.2(SPTB):c.1182+2T>C Single nucleotide variant Chr14:64797727 Likely pathogenic Splice donor variant rs2139613101 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001355436.2(SPTB):c.2519G>A (p.Arg840His) Single nucleotide variant Chr14:64793144 Conflicting classifications of pathogenicity Missense variant rs146326769 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001355436.2(SPTB):c.3784_3787del (p.Lys1262fs) Deletion Chr14:64785605 - 64785608 Likely pathogenic Frameshift variant rs1594773586 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution