GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Hereditary breast ovarian cancer syndrome

An  Autosomal dominant  mode(s) within the Cancer disorders  category

Conflicting classifications of pathogenicity 8
Likely pathogenic 2
Pathogenic 3
Pathogenic/Likely pathogenic 5
Uncertain significance 4

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_007294.4(BRCA1):c.2295del (p.Ser766fs) Deletion Chr17:43093236 Pathogenic/Likely pathogenic Frameshift variant|intron variant rs1567796243
NM_007294.4(BRCA1):c.3785_3787del (p.Ser1262del) Deletion Chr17:43091744 - 43091746 Uncertain significance Inframe_indel|inframe_deletion|intron variant rs1555587043
NM_007294.4(BRCA1):c.1574T>C (p.Val525Ala) Single nucleotide variant Chr17:43093957 Conflicting classifications of pathogenicity Missense variant|intron variant rs879253902
NM_007294.4(BRCA1):c.341C>G (p.Ser114Cys) Single nucleotide variant Chr17:43104222 Uncertain significance Missense variant|non-coding transcript variant rs786202620
NM_007294.4(BRCA1):c.3327_3329del (p.Lys1110del) Deletion Chr17:43092202 - 43092204 Conflicting classifications of pathogenicity Inframe_indel|inframe_deletion|intron variant rs80357575
NM_007294.4(BRCA1):c.5558A>G (p.Tyr1853Cys) Single nucleotide variant Chr17:43045712 Pathogenic/Likely pathogenic Missense variant|3 prime UTR variant|non-coding transcript variant rs80357258
NM_007294.4(BRCA1):c.5215G>T (p.Asp1739Tyr) Single nucleotide variant Chr17:43057114 Likely pathogenic Missense variant|non-coding transcript variant rs80357283 .Molecular Endocrinology Laboratory, Christian Medical College
NM_007294.4(BRCA1):c.3328_3330del (p.Lys1110del) Deletion Chr17:43092201 - 43092203 Conflicting classifications of pathogenicity Inframe_deletion|intron variant rs80358335 .Molecular Endocrinology Laboratory, Christian Medical College
NM_007294.4(BRCA1):c.182G>A (p.Cys61Tyr) Single nucleotide variant Chr17:43106486 Pathogenic Missense variant|non-coding transcript variant rs80357093
NM_007294.4(BRCA1):c.4484+1G>A Single nucleotide variant Chr17:43076487 Pathogenic Splice donor variant|intron variant rs80358063 .Bioinformatics dept., Datar Cancer Genetics Limited, India
NM_000059.4(BRCA2):c.5420dup (p.Asp1807fs) Duplication Chr13:32339774 - 32339775 Pathogenic Frameshift variant|non-coding transcript variant|intron variant rs2548530767 .Biotechnology, Institute of Science, Nirma University
NM_000059.4(BRCA2):c.4733T>G (p.Leu1578Ter) Single nucleotide variant Chr13:32339088 Pathogenic/Likely pathogenic Nonsense rs2137509604 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000059.4(BRCA2):c.3350T>C (p.Ile1117Thr) Single nucleotide variant Chr13:32337705 Conflicting classifications of pathogenicity Missense variant rs558973276
NM_000059.4(BRCA2):c.6952C>G (p.Arg2318Gly) Single nucleotide variant Chr13:32346841 Uncertain significance Missense variant rs80358920 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000059.4(BRCA2):c.5683G>A (p.Glu1895Lys) Single nucleotide variant Chr13:32340038 Conflicting classifications of pathogenicity Missense variant rs146351301 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000059.4(BRCA2):c.6112C>T (p.His2038Tyr) Single nucleotide variant Chr13:32340467 Conflicting classifications of pathogenicity Missense variant rs587778123
NM_000059.4(BRCA2):c.-26G>T Single nucleotide variant Chr13:32316435 Uncertain significance 5 prime UTR variant rs1799943
NM_000059.4(BRCA2):c.6152A>G (p.Asn2051Ser) Single nucleotide variant Chr13:32340507 Conflicting classifications of pathogenicity Missense variant rs398122549
NM_000059.4(BRCA2):c.8954-3C>G Single nucleotide variant Chr13:32379747 Likely pathogenic Intron variant rs81002844 .Biotechnology, Institute of Science, Nirma University
NM_000059.4(BRCA2):c.10089A>G (p.Ile3363Met) Single nucleotide variant Chr13:32398602 Conflicting classifications of pathogenicity Missense variant rs80358390 .Molecular Diagnostics, Rajiv Gandhi Cancer Institute & Research Center
NM_000059.4(BRCA2):c.476-1G>A Single nucleotide variant Chr13:32326241 Pathogenic/Likely pathogenic Splice acceptor variant rs397507340 .Biotechnology, Institute of Science, Nirma University
NM_058216.3(RAD51C):c.571+1del Deletion Chr17:58696858 Pathogenic/Likely pathogenic Splice donor variant rs1327086366 .Lifecell International Pvt. Ltd

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution