GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 582 of 1004 Rare Genetic Disorders of GenTIGS

Generalized epilepsy with febrile seizures plus, type 2

An  Autosomal dominant  mode(s) within the Neuronal disorders  category

Conflicting classifications of pathogenicity 2
Likely pathogenic 3
Pathogenic 13
Pathogenic/Likely pathogenic 3
Uncertain significance 5

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001165963.4(SCN1A):c.4003-1G>C Single nucleotide variant Chr2:166002754 Pathogenic Splice acceptor variant rs1574007140 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001165963.4(SCN1A):c.5624_5630del (p.Val1875fs) Deletion Chr2:165991645 - 165991651 Likely pathogenic Frameshift variant|non-coding transcript variant rs2105425236 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.5120T>C (p.Phe1707Ser) Single nucleotide variant Chr2:165992155 Pathogenic Missense variant|non-coding transcript variant rs2105432236 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001165963.4(SCN1A):c.4002+1G>T Single nucleotide variant Chr2:166009718 Pathogenic/Likely pathogenic Splice donor variant rs1692153643 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.5501C>T (p.Ala1834Val) Single nucleotide variant Chr2:165991774 Conflicting classifications of pathogenicity Missense variant|non-coding transcript variant rs780809852 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.4547C>A (p.Ser1516Ter) Single nucleotide variant Chr2:165996047 Pathogenic Nonsense|non-coding transcript variant rs139300715 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_001165963.4(SCN1A):c.4223G>A (p.Trp1408Ter) Single nucleotide variant Chr2:166002533 Pathogenic Nonsense|non-coding transcript variant rs794726784 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.5536_5539del (p.Lys1846fs) Microsatellite Chr2:165991736 - 165991739 Pathogenic Frameshift variant|non-coding transcript variant rs794726726 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.4906C>T (p.Arg1636Ter) Single nucleotide variant Chr2:165992369 Pathogenic Nonsense|non-coding transcript variant rs199727342 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.2589+2dup Duplication Chr2:166039420 - 166039421 Pathogenic/Likely pathogenic Splice donor variant rs2468112683 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.265del (p.Thr89fs) Deletion Chr2:166058688 Likely pathogenic Frameshift variant|5 prime UTR variant|non-coding transcript variant rs2105918665 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.2164A>C (p.Asn722His) Single nucleotide variant Chr2:166042304 Uncertain significance Missense variant|5 prime UTR variant|non-coding transcript variant rs1341631584 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.1719C>G (p.Ser573Arg) Single nucleotide variant Chr2:166043993 Uncertain significance Missense variant|5 prime UTR variant|non-coding transcript variant rs748767737 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.1037C>T (p.Pro346Leu) Single nucleotide variant Chr2:166047760 Likely pathogenic Missense variant|5 prime UTR variant|non-coding transcript variant rs2105868295 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001165963.4(SCN1A):c.1133del (p.Leu378fs) Deletion Chr2:166047664 Pathogenic/Likely pathogenic Frameshift variant|non-coding transcript variant|5 prime UTR variant rs1698004184 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
.Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.2006C>T (p.Pro669Leu) Single nucleotide variant Chr2:166043706 Uncertain significance Missense variant|5 prime UTR variant|non-coding transcript variant|intron variant rs570326929 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.36del (p.Asp12fs) Deletion Chr2:166073586 Pathogenic Frameshift variant|5 prime UTR variant|non-coding transcript variant rs1684704927 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_001165963.4(SCN1A):c.242A>G (p.Asp81Gly) Single nucleotide variant Chr2:166073380 Conflicting classifications of pathogenicity Missense variant|5 prime UTR variant|non-coding transcript variant rs1684663181 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_001165963.4(SCN1A):c.136G>A (p.Glu46Lys) Single nucleotide variant Chr2:166073486 Uncertain significance Missense variant|5 prime UTR variant|non-coding transcript variant rs769582667 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.2552A>G (p.Asn851Ser) Single nucleotide variant Chr2:166039460 Uncertain significance Missense variant|non-coding transcript variant rs561912072 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_001165963.4(SCN1A):c.602+1G>A Single nucleotide variant Chr2:166054637 Pathogenic Splice donor variant rs794726827 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_001165963.4(SCN1A):c.2589+3A>T Single nucleotide variant Chr2:166039420 Pathogenic Intron variant rs794726775 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.2134C>T (p.Arg712Ter) Single nucleotide variant Chr2:166042334 Pathogenic Nonsense|5 prime UTR variant|non-coding transcript variant rs794726730 .Lifecell International Pvt. Ltd
.Neuberg Centre For Genomic Medicine, NCGM
NM_001165963.4(SCN1A):c.272T>C (p.Ile91Thr) Single nucleotide variant Chr2:166058681 Pathogenic Missense variant|5 prime UTR variant|non-coding transcript variant rs121918734 .Lifecell International Pvt. Ltd
NM_001165963.4(SCN1A):c.677C>T (p.Thr226Met) Single nucleotide variant Chr2:166052869 Pathogenic Missense variant|5 prime UTR variant|non-coding transcript variant rs121917984 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001165963.4(SCN1A):c.302G>A (p.Arg101Gln) Single nucleotide variant Chr2:166058651 Pathogenic Missense variant|5 prime UTR variant|non-coding transcript variant rs121917918 .Lifecell International Pvt. Ltd

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution