GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Finnish congenital nephrotic syndrome

An  Autosomal recessive  mode(s) within the Nephrological disorders  category

Likely pathogenic 1
Pathogenic 1
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_004646.4(NPHS1):c.3061G>T (p.Asp1021Tyr) Single nucleotide variant Chr19:35839285 Uncertain significance Missense variant .Genetics laboratory, Department of Obstetrics & Gynae, Institute of Kidney Diseases & Research Centre Dr. H.L. Trivedi Institute Of Transplantation Sciences
NM_004646.4(NPHS1):c.2206G>A (p.Val736Met) Single nucleotide variant Chr19:35844109 Likely pathogenic Missense variant rs1131692245 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_004646.4(NPHS1):c.1099C>T (p.Arg367Cys) Single nucleotide variant Chr19:35848708 Pathogenic/Likely pathogenic Missense variant rs386833865 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_004646.4(NPHS1):c.3478C>T (p.Arg1160Ter) Single nucleotide variant Chr19:35831056 Pathogenic Nonsense rs267606919 .Genetics laboratory, Department of Obstetrics & Gynae, Institute of Kidney Diseases & Research Centre Dr. H.L. Trivedi Institute Of Transplantation Sciences
.Neuberg Centre For Genomic Medicine, NCGM

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution