GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Fetal akinesia deformation sequence 3

An  Autosomal recessive  mode(s) within the Respiratory disorders  category

Likely pathogenic 2
Pathogenic/Likely pathogenic 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001367561.1(DOCK7):c.1511_1513del (p.Pro504_Ile505delinsLeu) Deletion Chr1:62619906 - 62619908 Likely pathogenic Inframe_indel rs2522881217 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_173660.5(DOK7):c.68G>A (p.Trp23Ter) Single nucleotide variant Chr4:3463519 Likely pathogenic Nonsense rs2109312461 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_173660.5(DOK7):c.1378dup (p.Gln460fs) Duplication Chr4:3493358 - 3493359 Pathogenic/Likely pathogenic 3 prime UTR variant|frameshift variant rs606231133 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_173660.5(DOK7):c.1263dup (p.Ser422fs) Duplication Chr4:3493242 - 3493243 Pathogenic/Likely pathogenic Frameshift variant|3 prime UTR variant rs606231129 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution