GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Fetal akinesia deformation sequence 1

An  Autosomal recessive  mode(s) within the Respiratory disorders  category

Likely pathogenic 1
Pathogenic/Likely pathogenic 3

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_173660.5(DOK7):c.1511_1513del (p.Pro504_Ter505delinsArg) Deletion Chr4:3493497 - 3493499 Likely pathogenic 3 prime UTR variant|stop lost|intron variant rs762345055
NM_173660.5(DOK7):c.1378dup (p.Gln460fs) Duplication Chr4:3493358 - 3493359 Pathogenic/Likely pathogenic 3 prime UTR variant|frameshift variant rs606231133 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_173660.5(DOK7):c.1263dup (p.Ser422fs) Duplication Chr4:3493242 - 3493243 Pathogenic/Likely pathogenic Frameshift variant|3 prime UTR variant rs606231129 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_005055.5(RAPSN):c.490C>T (p.Arg164Cys) Single nucleotide variant Chr11:47447853 Pathogenic/Likely pathogenic Missense variant rs104894294 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution