GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Fanconi-Bickel syndrome

An  Autosomal recessive  mode(s) within the Metabolic disorders  category

Conflicting classifications of pathogenicity 1
Likely pathogenic 3
Pathogenic 3

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_000340.2(SLC2A2):c.469G>C (p.Gly157Arg) Single nucleotide variant Chr3:171009985 Conflicting classifications of pathogenicity Missense variant|intron variant rs750836049 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000340.2(SLC2A2):c.613-7T>G Single nucleotide variant Chr3:171006112 Likely pathogenic Intron variant rs2108244550 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000340.2(SLC2A2):c.2T>G (p.Met1Arg) Single nucleotide variant Chr3:171026669 Pathogenic Missense variant|initiator_codon_variant|5 prime UTR variant rs1716716102 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000340.2(SLC2A2):c.589G>C (p.Val197Leu) Single nucleotide variant Chr3:171007171 Likely pathogenic Missense variant rs121909741 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000340.2(SLC2A2):c.1246G>A (p.Gly416Ser) Single nucleotide variant Chr3:170998321 Likely pathogenic Missense variant rs1553785033 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_000340.2(SLC2A2):c.952G>A (p.Gly318Arg) Single nucleotide variant Chr3:171005296 Pathogenic Missense variant rs780067980 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
NM_000340.2(SLC2A2):c.1093C>T (p.Arg365Ter) Single nucleotide variant Chr3:170999142 Pathogenic Nonsense rs121909742 .Laboratory of Cyto-molecular Genetics, Department of Anatomy, All India Institute of Medical Sciences (AIIMS), New Delhi
.Lifecell International Pvt. Ltd

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution