GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

Developmental and epileptic encephalopathy, 42

An  Autosomal dominant  mode(s) within the Neurodevelopmental disorders  category

Pathogenic 1
Pathogenic/Likely pathogenic 3
Uncertain significance 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001127222.2(CACNA1A):c.6901C>G (p.Pro2301Ala) Single nucleotide variant Chr19:13207933 Uncertain significance 3 prime UTR variant|missense variant rs1351010453 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_001127222.2(CACNA1A):c.1924G>A (p.Asp642Asn) Single nucleotide variant Chr19:13307844 Uncertain significance Missense variant rs2057938033 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_001127222.2(CACNA1A):c.4043G>A (p.Arg1348Gln) Single nucleotide variant Chr19:13262780 Pathogenic/Likely pathogenic Missense variant rs1057520918 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001127222.2(CACNA1A):c.653C>T (p.Ser218Leu) Single nucleotide variant Chr19:13365448 Pathogenic/Likely pathogenic Missense variant rs121908225 .Lifecell International Pvt. Ltd
NM_001127222.2(CACNA1A):c.4148A>G (p.Tyr1383Cys) Single nucleotide variant Chr19:13261552 Pathogenic/Likely pathogenic Missense variant rs121908219 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001127222.2(CACNA1A):c.1994C>T (p.Thr665Met) Single nucleotide variant Chr19:13303877 Pathogenic Missense variant rs121908212 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar