GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Deficiency of aromatic-L-amino-acid decarboxylase

An  Autosomal recessive  mode(s) within the Metabolic disorders  category

Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001082971.2(DDC):c.1040G>A (p.Arg347Gln) Single nucleotide variant Chr7:50476625 Pathogenic/Likely pathogenic Missense variant rs201951824 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001082971.2(DDC):c.353T>A (p.Met118Lys) Single nucleotide variant Chr7:50537942 Uncertain significance Missense variant|intron variant .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution