GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Crigler-Najjar syndrome type 1

An  Autosomal recessive  mode(s) within the Metabolic disorders  category

Conflicting classifications of pathogenicity; drug response; other 1
Conflicting classifications of pathogenicity; other 1
Pathogenic/Likely pathogenic 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
UGT1A1*28 Microsatellite Chr2:233760233 - 233760234 Conflicting classifications of pathogenicity; drug response; other Intron variant rs3064744 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_000463.3(UGT1A1):c.353dup (p.Asp119fs) Duplication Chr2:233760634 - 233760635 Pathogenic/Likely pathogenic Frameshift variant|intron variant rs748219743 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
.Neuberg Centre For Genomic Medicine, NCGM
NM_000463.3(UGT1A1):c.1091C>T (p.Pro364Leu) Single nucleotide variant Chr2:233768226 Conflicting classifications of pathogenicity; other Missense variant rs34946978

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution