GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 496 rare genetic disorders, with a total of 857 reported, submitted from India

Congenital myopathy

An   mode(s) within the Neuromuscular disorders  category

Likely pathogenic 1
Pathogenic 1
Pathogenic/Likely pathogenic 3
Uncertain significance 1

Variant name Variant type Germline classification Molecular consequence Grch38 Location dbSNP_ID Submitter
NM_001100.4(ACTA1):c.977_979dup (p.Thr326_Met327insThr) Duplication Uncertain significance inframe_insertion Chr1:229431731 - 229431732 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_000069.3(CACNA1S):c.1583G>A (p.Arg528His) single nucleotide variant Pathogenic missense variant Chr1:201077915 rs80338777 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_000083.3(CLCN1):c.1437_1450del (p.Pro480fs) Deletion Pathogenic/Likely pathogenic frameshift variant|non-coding transcript variant Chr7:143339287 - 143339300 rs768119034
NM_000083.3(CLCN1):c.2680C>T (p.Arg894Ter) single nucleotide variant Pathogenic/Likely pathogenic nonsense|non-coding transcript variant Chr7:143351678 rs55960271
NM_000540.3(RYR1):c.9847C>T (p.Arg3283Ter) single nucleotide variant Pathogenic/Likely pathogenic nonsense Chr19:38517520 rs752199191 .Lifecell International Pvt. Ltd
NM_152263.4(TPM3):c.654AGA[1] (p.Glu219del) Microsatellite Likely pathogenic inframe_deletion|non-coding transcript variant|intron variant Chr1:154170695 - 154170697 rs876661407 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar