GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Chorea-acanthocytosis

An  Autosomal recessive  mode(s) within the Neurodegenerative disorders  category

Likely pathogenic 1
Pathogenic 2
Pathogenic/Likely pathogenic 1
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_033305.3(VPS13A):c.495+4_495+7del Deletion Chr9:77209533 - 77209536 Uncertain significance Splice donor variant .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_033305.3(VPS13A):c.9263T>G (p.Met3088Arg) Single nucleotide variant Chr9:77403309 Likely pathogenic rs2538311239 .Department of Cell and Molecular Biology, Manipal School of Life Sciences, Manipal Academy of Higher Education
NM_033305.3(VPS13A):c.4918C>T (p.Gln1640Ter) Single nucleotide variant Chr9:77317660 Pathogenic Nonsense rs1829478568 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_033305.3(VPS13A):c.555+1G>A Single nucleotide variant Chr9:77210676 Pathogenic/Likely pathogenic Splice donor variant rs1590003601 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_033305.3(VPS13A):c.799C>T (p.Arg267Ter) Single nucleotide variant Chr9:77219998 Pathogenic Nonsense rs771004767 .Department of Cell and Molecular Biology, Manipal School of Life Sciences, Manipal Academy of Higher Education

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution