GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Variants from 536 rare genetic disorders, with a total of 897 reported, submitted from India

CHARGE syndrome

An  Autosomal dominant  mode(s) within the Multisystemic disorders  category

Likely pathogenic 3
Pathogenic 4
Pathogenic/Likely pathogenic 2
Uncertain significance 1

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_017780.4(CHD7):c.619C>T (p.Gln207Ter) Single nucleotide variant Chr8:60742051 Pathogenic Nonsense rs2487267049 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_017780.4(CHD7):c.2333C>G (p.Ala778Gly) Single nucleotide variant Chr8:60800482 Uncertain significance Missense variant|intron variant rs747595218 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
NM_017780.4(CHD7):c.3757_3778+7del Deletion Chr8:60830554 - 60830582 Likely pathogenic Splice donor variant|intron variant rs2487855072 .Lifecell International Pvt. Ltd
NM_017780.4(CHD7):c.5480del (p.Lys1827fs) Deletion Chr8:60850567 Likely pathogenic Frameshift variant|intron variant rs2488015610 .Lifecell International Pvt. Ltd
NM_017780.4(CHD7):c.7803C>G (p.Tyr2601Ter) Single nucleotide variant Chr8:60861098 Pathogenic/Likely pathogenic Nonsense|intron variant rs1563669432 .Lifecell International Pvt. Ltd
NM_017780.4(CHD7):c.5504_5508delinsT (p.Gly1835fs) Indel Chr8:60850592 - 60850596 Likely pathogenic Frameshift variant|intron variant rs1586440620 .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_017780.4(CHD7):c.3106C>T (p.Arg1036Ter) Single nucleotide variant Chr8:60822651 Pathogenic Nonsense|intron variant rs1554597716 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_017780.4(CHD7):c.1735C>T (p.Gln579Ter) Single nucleotide variant Chr8:60781069 Pathogenic/Likely pathogenic Nonsense|intron variant rs780953224 .Lifecell International Pvt. Ltd
NM_017780.4(CHD7):c.5833C>T (p.Arg1945Ter) Single nucleotide variant Chr8:60852186 Pathogenic Nonsense|intron variant rs757160222 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_017780.4(CHD7):c.2959C>T (p.Arg987Ter) Single nucleotide variant Chr8:60822504 Pathogenic Nonsense|intron variant rs886040983 .Lifecell International Pvt. Ltd

Graph displaying all Indian institutes, the rare genetic disorders they studied, and the variants submitted to ClinVar