GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Autosomal recessive juvenile Parkinson disease 2

An  Autosomal recessive  mode(s) within the Neurodegenerative disorders  category

Likely pathogenic 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_001018111.3(PODXL):c.89_90insGTCGCCCC (p.Gln32fs) Insertion Chr7:131556270 - 131556271 Likely pathogenic Frameshift variant rs1554391082 .Prof. Thelma's Laboratory, Department of Genetics, University of Delhi South Campus
NM_004562.3(PRKN):c.1301T>C (p.Met434Thr) Single nucleotide variant Chr6:161350196 Likely pathogenic Missense variant rs1582953433 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution