GenTIGSA Gene Database on Rare Genetic Disorders

Variants in ClinVar from 539 of 916 Rare Genetic Disorders of GenTIGS

Arthrogryposis multiplex congenita

An  Autosomal dominant, Autosomal recessive, X-linked dominant  mode(s) within the Neuromuscular disorders  category

Likely pathogenic 4
Pathogenic 4
Pathogenic/Likely pathogenic 1
Uncertain significance 2

Variant name Variant type GRCH38 location Germline classification Molecular consequence dbSNP_ID Submitter
NM_139284.3(LGI4):c.2T>C (p.Met1Thr) Single nucleotide variant Chr19:35134679 Pathogenic Missense variant|initiator_codon_variant rs1207534366 .Department of Medical Genetics, Sanjay Gandhi Post Graduate Institute of Medical Sciences
NM_002478.5(MYOD1):c.557dup (p.Arg188fs) Duplication Chr11:17720334 - 17720335 Pathogenic Frameshift variant rs1179926739 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_001164508.2(NEB):c.10170G>A (p.Trp3390Ter) Single nucleotide variant Chr2:151627179 Likely pathogenic Nonsense rs1560619891 .Lifecell International Pvt. Ltd
NM_001164508.2(NEB):c.9102+1G>C Single nucleotide variant Chr2:151636226 Likely pathogenic Intron variant|splice donor variant rs143644938 .Lifecell International Pvt. Ltd
NM_001164508.2(NEB):c.16809C>A (p.Asp5603Glu) Single nucleotide variant Chr2:151576250 Uncertain significance Missense variant rs1359484405 .Pediatrics Genetics, Post Graduate Institute of Medical Education and Research
NM_001164508.2(NEB):c.11164C>T (p.Arg3722Ter) Single nucleotide variant Chr2:151617381 Pathogenic/Likely pathogenic Nonsense rs928945364 .Lifecell International Pvt. Ltd
NM_001164508.2(NEB):c.3255+1G>A Single nucleotide variant Chr2:151679720 Pathogenic Splice donor variant rs375628303 .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
.Neuberg Centre For Genomic Medicine, NCGM
NM_017988.6(SCYL2):c.1748TTAATC[1] (p.583LN[1]) Microsatellite Chr12:100329302 - 100329307 Uncertain significance .Kasturba Medical College, Manipal, Kasturba Medical College, Manipal, Manipal Academy of Higher Education, Manipal, India
NM_017988.6(SCYL2):c.214_234del (p.Asp72_Glu78del) Deletion Chr12:100291539 - 100291559 Pathogenic Inframe_deletion|5 prime UTR variant rs2500017861 .Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
NM_020654.5(SENP7):c.3088C>T (p.Arg1030Trp) Single nucleotide variant Chr3:101326008 Likely pathogenic Missense variant .Diagnostics Services (NGS), CSIR - Centre For Cellular And Molecular Biology
NM_000113.3(TOR1A):c.844C>T (p.Arg282Ter) Single nucleotide variant Chr9:129814127 Likely pathogenic Nonsense rs753220814 .Division of Medical Genetics, Department of Pediatrics, All India Institute of Medical Sciences, New Delhi
.Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics

Indian Institutes & Variant Submission Overview
Chromosome-wise Variant Distribution