GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Monogenic disorders list  

List of monogenic disorders and their associated genes
Monogenic disorders arise from mutations in a single gene, but variations within that gene or in multiple genes can also lead to similar phenotypes, typically following Mendelian inheritance patterns associated with specific genetic changes.

View information by inheritance mode


S.No.  Genetic Disorders
Modes of inheritance
Category Gene symbol Indian
context
 Links
581 X-linked lissencephaly with abnormal genitalia 
X-linked recessive
Multisystemic disorders ARX aristaless related homeobox
Reports
Updated as of Nov 12, 2025
PubMed
582 X-linked lymphoproliferative disease due to SH2D1A deficiency 
X-linked recessive
Immune disorders SH2D1A SH2 domain containing 1A
Reports
Updated as of Feb 10, 2026
PubMed
583 X-linked myopathy with excessive autophagy 
X-linked recessive
Neuromuscular disorders VMA21 vacuolar ATPase assembly factor VMA21
Reports
Updated as of Feb 01, 2025
PubMed