GenTIGSA Gene Database on Rare Genetic Disorders
  Beta Version

Monogenic disorders list  

List of monogenic disorders and their associated genes
Monogenic disorders arise from mutations in a single gene, but variations within that gene or in multiple genes can also lead to similar phenotypes, typically following Mendelian inheritance patterns associated with specific genetic changes.

View information by inheritance mode


S.No.  Genetic Disorders
Modes of inheritance
Category Gene symbol Indian
context
 Links
361 Mucolipidosis type II 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders GNPTAB N-acetylglucosamine-1-phosphate transferase subunits alpha and beta
Reports
Updated as of May 24, 2023
PubMed
362 Mucolipidosis type IV 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders MCOLN1 mucolipin TRP cation channel 1
Reports
Updated as of Mar 30, 2026
PubMed
363 Mucopolysaccharidosis type 1 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders IDUA alpha-L-iduronidase
Reports
Updated as of Feb 26, 2025
PubMed
364 Mucopolysaccharidosis type 2 
X-linked dominant
Metabolic disorders/Lysosomal storage disorders IDS iduronate 2-sulfatase
Reports
Updated as of May 24, 2023
PubMed
365 Mucopolysaccharidosis type 7 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders GUSB glucuronidase beta
Reports
Updated as of Feb 01, 2025
PubMed
366 Mucopolysaccharidosis, MPS-I-S 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders IDUA alpha-L-iduronidase
Reports
Updated as of Sep 08, 2025
PubMed
367 Mucopolysaccharidosis, MPS-IV-A 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders GALNS galactosamine (N-acetyl)-6-sulfatase
Reports
Updated as of Sep 05, 2023
PubMed
368 Mucosa-associated lymphoma 
Cancer disorders BCL10 BCL10 immune signaling adaptor
Reports
Updated as of Feb 01, 2024
PubMed
369 Muenke syndrome 
Autosomal dominant
Bone disorders FGFR3 fibroblast growth factor receptor 3
Reports
Updated as of Feb 01, 2024
PubMed
370 Mulibrey nanism syndrome 
Autosomal recessive
Bone disorders TRIM37 tripartite motif containing 37
Reports
Updated as of Feb 01, 2024
PubMed