GenTIGSA Gene Database on Rare Genetic Disorders

Monogenic disorders list  

List of monogenic disorders and their associated genes
Monogenic disorders arise from mutations in a single gene, but variations within that gene or in multiple genes can also lead to similar phenotypes, typically following Mendelian inheritance patterns associated with specific genetic changes.

View information by inheritance mode


S.No.  Genetic Disorders
Modes of inheritance
Category Gene symbol Indian
context
 Links
281 Metatropic dysplasia 
Autosomal dominant
Bone disorders TRPV4 transient receptor potential cation channel subfamily V member 4
Reports
Updated as of Feb 01, 2024
PubMed
282 Mevalonic aciduria 
Autosomal recessive
Metabolic disorders MVK mevalonate kinase
Reports
Updated as of Feb 01, 2024
PubMed
283 Microcephaly 5, primary, autosomal recessive 
Autosomal recessive
Neurodevelopmental disorders ASPM assembly factor for spindle microtubules
Reports
Updated as of Feb 01, 2025
PubMed
284 Microcephaly, normal intelligence and immunodeficiency 
Autosomal recessive
Immune disorders NBN nibrin
Reports
Updated as of Feb 26, 2025
PubMed
285 Miller syndrome 
Autosomal recessive
Bone disorders DHODH dihydroorotate dehydrogenase (quinone)
Reports
Updated as of Jan 04, 2024
PubMed
286 Mitochondrial DNA depletion syndrome 6 (hepatocerebral type) 
Autosomal recessive
Metabolic disorders MPV17 mitochondrial inner membrane protein MPV17
Reports
Updated as of Jul 20, 2024
PubMed
287 Monomelic amyotrophy 
Neuromuscular disorders SLIT1 slit guidance ligand 1
Reports
Updated as of Feb 01, 2024
PubMed
288 Morning glory disc anomaly 
Autosomal dominant
Eye disorders PAX6 paired box 6
Reports
Updated as of Jan 04, 2024
PubMed
289 Mosaic variegated aneuploidy syndrome 2 
Autosomal recessive
Multisystemic disorders CEP57 centrosomal protein 57
Reports
Updated as of Feb 01, 2024
PubMed
290 Mucolipidosis type II 
Autosomal recessive
Metabolic disorders/Lysosomal storage disorders GNPTAB N-acetylglucosamine-1-phosphate transferase subunits alpha and beta
Reports
Updated as of May 24, 2023
PubMed