GenTIGSA Gene Database on Rare Genetic Disorders

Prominin 1 (PROM1) Associated conditions:  1. Usher syndrome  2. Retinitis pigmentosa  3. Leber congenital amaurosis  4. Stargardt disease 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001441173.1 NP_001428102.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED NR_199807.1 - NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
3 REVIEWED NR_199806.1 - NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
4 REVIEWED NM_006017.3 NP_006008.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
5 REVIEWED NM_001441179.1 NP_001428108.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
6 REVIEWED NM_001441178.1 NP_001428107.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
7 REVIEWED NM_001441177.1 NP_001428106.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
8 REVIEWED NM_001441176.1 NP_001428105.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
9 REVIEWED NM_001441175.1 NP_001428104.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
10 REVIEWED NM_001441174.1 NP_001428103.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
11 REVIEWED NM_001145847.2 NP_001139319.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
12 REVIEWED NM_001371408.1 NP_001358337.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
13 REVIEWED NM_001371407.1 NP_001358336.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
14 REVIEWED NM_001371406.1 NP_001358335.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
15 REVIEWED NM_001145852.2 NP_001139324.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
16 REVIEWED NM_001145851.2 NP_001139323.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
17 REVIEWED NM_001145850.2 NP_001139322.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
18 REVIEWED NM_001145849.2 NP_001139321.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -
19 REVIEWED NM_001145848.2 NP_001139320.1 NC_000004.12 (15968227..16084022, complement) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1631 reference articles

Variant Information Prominin 1 (PROM1Mutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Prominin 1 (PROM1)
ClinVar variants:Revealing mutagenic patterns

GO Term of Prominin 1 (PROM1)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAlocated_inphotoreceptor outer segmentComponent
2Homo sapiensISSlocated_inphotoreceptor outer segmentComponent
3Homo sapiensIPIenablesprotein bindingFunction18654668 23084749 24556617 
4Homo sapiensHDAlocated_inextracellular spaceComponent16502470 
5Homo sapiensIDAlocated_inendoplasmic reticulumComponent24556617 
6Homo sapiensIEAlocated_inendoplasmic reticulumComponent
7Homo sapiensIDAlocated_inendoplasmic reticulum-Golgi intermediate compartmentComponent24556617 
8Homo sapiensIEAlocated_inendoplasmic reticulum-Golgi intermediate compartmentComponent
9Homo sapiensIDAlocated_inplasma membraneComponent12042327 24556617 
10Homo sapiensTASlocated_inplasma membraneComponent9389720 
11Homo sapiensIBAis_active_inmicrovillusComponent
12Homo sapiensIBAis_active_inciliumComponent
13Homo sapiensIDAlocated_incell surfaceComponent16809613 19384922 
14Homo sapiensISSinvolved_inretina layer formationProcess
15Homo sapiensIEAlocated_inmembraneComponent
16Homo sapiensIBAis_active_inapical plasma membraneComponent
17Homo sapiensIEAlocated_inapical plasma membraneComponent
18Homo sapiensIEAlocated_inmicrovillus membraneComponent
19Homo sapiensHDAlocated_invesicleComponent19190083 
20Homo sapiensIBAinvolved_inmicrovillus organizationProcess
21Homo sapiensIDAlocated_inphotoreceptor outer segment membraneComponent18654668 
22Homo sapiensIDAenablesactinin bindingFunction18654668 
23Homo sapiensIPIenablescadherin bindingFunction18654668 
24Homo sapiensIMPinvolved_inphotoreceptor cell maintenanceProcess18654668 
25Homo sapiensIMPinvolved_inretina morphogenesis in camera-type eyeProcess18654668 
26Homo sapiensIBAinvolved_incamera-type eye photoreceptor cell differentiationProcess
27Homo sapiensIMPinvolved_incamera-type eye photoreceptor cell differentiationProcess18654668 
28Homo sapiensISSinvolved_incamera-type eye photoreceptor cell differentiationProcess
29Homo sapiensHDAlocated_inextracellular exosomeComponent19056867 19199708 23533145 
30Homo sapiensIDAlocated_inextracellular exosomeComponent21082674 
31Homo sapiensIBAis_active_inprominosomeComponent
32Homo sapiensIMPinvolved_inpodocyte differentiationProcess19092120 
33Homo sapiensIMPinvolved_inglomerular parietal epithelial cell differentiationProcess19092120 
34Homo sapiensIMPinvolved_inpositive regulation of nephron tubule epithelial cell differentiationProcess16885410