GenTIGSA Gene Database on Rare Genetic Disorders

Tectonic family member 1 (TCTN1) Associated conditions:  1. Joubert syndrome 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001082537.3 NP_001076006.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
2 REVIEWED NM_001082538.3 NP_001076007.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
3 REVIEWED NM_001173975.3 NP_001167446.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
4 REVIEWED NM_001173976.2 NP_001167447.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
5 REVIEWED NM_001319680.2 NP_001306609.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
6 REVIEWED NM_001319681.2 NP_001306610.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
7 REVIEWED NM_001319682.3 NP_001306611.1 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
8 REVIEWED NM_024549.6 NP_078825.2 NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58
9 REVIEWED NR_135088.2 - NC_000012.12 (110614128..110649429) Reference GRCh38.p14 Primary Assembly Q2MV58

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 127 reference articles

Variant Information Tectonic family member 1 (TCTN1Mutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Tectonic family member 1 (TCTN1)
ClinVar variants:Revealing mutagenic patterns

GO Term of Tectonic family member 1 (TCTN1)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAinvolved_inin utero embryonic developmentProcess
2Homo sapiensIEAinvolved_inneural tube formationProcess
3Homo sapiensIEAlocated_inextracellular spaceComponent
4Homo sapiensTASlocated_incytosolComponent
5Homo sapiensIEAlocated_incytoskeletonComponent
6Homo sapiensIEAinvolved_inregulation of smoothened signaling pathwayProcess
7Homo sapiensIEAlocated_inmembraneComponent
8Homo sapiensIEAinvolved_insomatic motor neuron differentiationProcess
9Homo sapiensIEAinvolved_intelencephalon developmentProcess
10Homo sapiensIEAinvolved_indorsal/ventral neural tube patterningProcess
11Homo sapiensIEAinvolved_incentral nervous system interneuron axonogenesisProcess
12Homo sapiensIBApart_ofMKS complexComponent21873635 
13Homo sapiensISSpart_ofMKS complexComponent
14Homo sapiensIBAinvolved_incilium assemblyProcess21873635 
15Homo sapiensISSinvolved_incilium assemblyProcess
16Homo sapiensIBAinvolved_inprotein localization to ciliary transition zoneProcess21873635