GenTIGSA Gene Database on Rare Genetic Disorders

Peripherin 2 (PRPH2) Associated conditions:  1. Retinitis pigmentosa  2. Stargardt disease 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_000322.5 NP_000313.2 NC_000006.12 (42696597..42722596, complement) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED XR_007059288.1 - NC_000006.12 (42696597..42722596, complement) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1121 reference articles

Variant Information Peripherin 2 (PRPH2Mutation Visualization Dashboard: Pathogenic variant distribution chart
ClinVar variants:Revealing mutagenic patterns

GO Term of Peripherin 2 (PRPH2)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAlocated_inphotoreceptor outer segmentComponent
2Homo sapiensIEAlocated_inphotoreceptor inner segmentComponent
3Homo sapiensIPIenablesprotein bindingFunction32814053 
4Homo sapiensIBAis_active_inplasma membraneComponent
5Homo sapiensIEAinvolved_incell adhesionProcess
6Homo sapiensIEAinvolved_invisual perceptionProcess
7Homo sapiensTASinvolved_invisual perceptionProcess1749427 
8Homo sapiensIEAinvolved_inresponse to low light intensity stimulusProcess
9Homo sapiensIEAlocated_inmembraneComponent
10Homo sapiensTASlocated_inmembraneComponent1749427 
11Homo sapiensIEAenablesprotein homodimerization activityFunction
12Homo sapiensIBAinvolved_inprotein maturationProcess
13Homo sapiensIBAinvolved_inprotein localization to plasma membraneProcess