GenTIGSA Gene Database on Rare Genetic Disorders

Protein O-linked mannose N-acetylglucosaminyltransferase 1 (beta 1,2-) (POMGNT1) Associated conditions:  1. Muscle eye brain disease  2. Retinitis pigmentosa 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001243766.2 NP_001230695.2 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
2 REVIEWED NM_001290129.3 NP_001277058.2 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
3 REVIEWED NM_001290130.2 NP_001277059.2 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
4 REVIEWED NM_001410783.1 NP_001397712.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
5 REVIEWED NM_001437653.1 NP_001424582.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
6 REVIEWED NM_001438686.1 NP_001425615.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
7 REVIEWED NM_001438688.1 NP_001425617.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
8 REVIEWED NM_001438689.1 NP_001425618.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
9 REVIEWED NM_001438691.1 NP_001425620.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
10 REVIEWED NM_001438692.1 NP_001425621.1 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1
11 REVIEWED NM_017739.4 NP_060209.4 NC_000001.11 (46188682..46220304, complement) Reference GRCh38.p14 Primary Assembly Q8WZA1

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 172 reference articles

Variant Information Protein O-linked mannose N-acetylglucosaminyltransferase 1 (beta 1,2-) (POMGNT1Mutation Visualization Dashboard: Pathogenic variant distribution chart
ClinVar variants:Revealing mutagenic patterns

GO Term of Protein O-linked mannose N-acetylglucosaminyltransferase 1 (beta 1,2-) (POMGNT1)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIBAis_active_inGolgi membraneComponent
2Homo sapiensIDAlocated_inGolgi membraneComponent17034757 
3Homo sapiensIEAlocated_inGolgi membraneComponent
4Homo sapiensTASlocated_inGolgi membraneComponent
5Homo sapiensIPIenablesprotein bindingFunction17034757 25416956 28514442 
29892012 32296183 32707033 
33961781 
6Homo sapiensIDAacts_upstream_of_or_withinprotein O-linked glycosylationProcess11709191 
7Homo sapiensIEAinvolved_inprotein O-linked glycosylationProcess
8Homo sapiensIMPinvolved_inprotein O-linked glycosylationProcess26908613 27391550 
9Homo sapiensIDAenablesacetylglucosaminyltransferase activityFunction27493216 
10Homo sapiensIEAenablesacetylglucosaminyltransferase activityFunction
11Homo sapiensIMPenablesacetylglucosaminyltransferase activityFunction26908613 27391550 
12Homo sapiensIEAinvolved_inglycoprotein biosynthetic processProcess
13Homo sapiensIMPlocated_inmembraneComponent27493216 
14Homo sapiensIBAinvolved_inprotein O-linked glycosylation via N-acetyl-galactosamineProcess
15Homo sapiensIDAinvolved_inprotein O-linked glycosylation via N-acetyl-galactosamineProcess27493216 
16Homo sapiensIEAenablestransferase activityFunction
17Homo sapiensIEAenablesglycosyltransferase activityFunction
18Homo sapiensIDAenablesmanganese ion bindingFunction27493216 
19Homo sapiensIEAenablescarbohydrate bindingFunction
20Homo sapiensIEAenablesmetal ion bindingFunction
21Homo sapiensIBAenablesbeta-1,3-galactosyl-O-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase activityFunction
22Homo sapiensIDAenablesbeta-1,3-galactosyl-O-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase activityFunction11742540 
23Homo sapiensTASenablesbeta-1,3-galactosyl-O-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase activityFunction