GenTIGSA Gene Database on Rare Genetic Disorders

Pyridoxamine 5'-phosphate oxidase (PNPO) Associated conditions:  1. Pyridoxal phosphate-responsive seizures 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_018129.4 NP_060599.1 NC_000017.11 (47941570..47949307) Reference GRCh38.p14 Primary Assembly V9HW45

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 147 reference articles

Variant Information Pyridoxamine 5'-phosphate oxidase (PNPOMutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Pyridoxamine 5'-phosphate oxidase (PNPO)
ClinVar variants:Revealing mutagenic patterns

GO Term of Pyridoxamine 5'-phosphate oxidase (PNPO)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIBAenablespyridoxamine phosphate oxidase activityFunction21873635 
2Homo sapiensIDAenablespyridoxamine phosphate oxidase activityFunction12824491 15772097 
3Homo sapiensIPIenablesprotein bindingFunction25910212 32296183 
4Homo sapiensTASlocated_incytosolComponent
5Homo sapiensIEAinvolved_inpyridoxine biosynthetic processProcess
6Homo sapiensIDAenablesFMN bindingFunction12824491 
7Homo sapiensIDAenablespyridoxal phosphate bindingFunction12824491 
8Homo sapiensIDAenablesprotein homodimerization activityFunction12824491 
9Homo sapiensIEAinvolved_inpyridoxamine metabolic processProcess
10Homo sapiensIBAinvolved_inpyridoxal phosphate biosynthetic processProcess21873635 
11Homo sapiensIDAinvolved_inpyridoxal phosphate biosynthetic processProcess12824491