GenTIGSA Gene Database on Rare Genetic Disorders

Abelson helper integration site 1 (AHI1) Associated conditions:  1. Retinitis pigmentosa  2. Joubert syndrome  3. Leber congenital amaurosis  4. Nephronophthisis 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001134830.2 NP_001128302.1 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED NM_001134831.2 NP_001128303.1 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
3 REVIEWED NM_001134832.2 NP_001128304.1 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
4 REVIEWED NM_001350503.2 NP_001337432.1 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
5 REVIEWED NM_001350504.2 NP_001337433.1 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
6 REVIEWED NM_017651.5 NP_060121.3 NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
7 REVIEWED XR_001743480.3 - NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
8 REVIEWED XR_007059276.1 - NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
9 REVIEWED XR_007059277.1 - NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -
10 REVIEWED XR_007059278.1 - NC_000006.12 (135283531..135497739, complement) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 189 reference articles

Variant Information Abelson helper integration site 1 (AHI1Mutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Abelson helper integration site 1 (AHI1)
ClinVar variants:Revealing mutagenic patterns

GO Term of Abelson helper integration site 1 (AHI1)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensISSinvolved_inpositive regulation of receptor internalizationProcess
2Homo sapiensIPIenablesprotein bindingFunction18633336 22623184 23532844 
25825872 
3Homo sapiensIDAlocated_incentrosomeComponent18633336 
4Homo sapiensIEAlocated_incentrioleComponent
5Homo sapiensISSlocated_incentrioleComponent
6Homo sapiensTASlocated_incytosolComponent
7Homo sapiensIDAlocated_incell-cell junctionComponent18633336 
8Homo sapiensIDAlocated_inadherens junctionComponent18633336 
9Homo sapiensIEAlocated_inadherens junctionComponent
10Homo sapiensIClocated_inciliumComponent21959375 
11Homo sapiensIDAlocated_inciliumComponent18633336 
12Homo sapiensISSlocated_inciliumComponent
13Homo sapiensISSinvolved_incell surface receptor protein tyrosine kinase signaling pathwayProcess
14Homo sapiensISSinvolved_inintracellular protein localizationProcess
15Homo sapiensISSinvolved_invesicle-mediated transportProcess
16Homo sapiensIEAinvolved_incell projection organizationProcess
17Homo sapiensIEAinvolved_incell differentiationProcess
18Homo sapiensISSinvolved_inphotoreceptor cell outer segment organizationProcess
19Homo sapiensNASlocated_inciliary transition zoneComponent22179047 
20Homo sapiensISSpart_ofMKS complexComponent
21Homo sapiensIBAis_active_inciliary basal bodyComponent
22Homo sapiensIDAlocated_inciliary basal bodyComponent18633336 
23Homo sapiensIPIenablesidentical protein bindingFunction23532844 
24Homo sapiensISSinvolved_innegative regulation of apoptotic processProcess
25Homo sapiensIBAinvolved_inmotile cilium assemblyProcess
26Homo sapiensISSinvolved_inpositive regulation of transcription by RNA polymerase IIProcess
27Homo sapiensISSinvolved_inregulation of behaviorProcess
28Homo sapiensIMPinvolved_incilium assemblyProcess21959375 
29Homo sapiensISSinvolved_incilium assemblyProcess
30Homo sapiensISSlocated_innon-motile ciliumComponent
31Homo sapiensNASinvolved_inprotein localization to ciliary transition zoneProcess22179047