GenTIGSA Gene Database on Rare Genetic Disorders

Propionyl-CoA carboxylase subunit alpha (PCCA) Associated conditions:  1. Propionic acidemia 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001352610.2 NP_001339539.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED XR_007063681.1 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
3 REVIEWED NR_148031.2 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
4 REVIEWED NR_148030.2 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
5 REVIEWED NR_148029.2 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
6 REVIEWED NR_148028.2 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
7 REVIEWED NR_148027.2 - NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
8 REVIEWED NM_001352612.2 NP_001339541.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
9 REVIEWED NM_001352611.2 NP_001339540.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
10 REVIEWED NM_000282.4 NP_000273.2 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
11 REVIEWED NM_001352609.2 NP_001339538.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
12 REVIEWED NM_001352608.2 NP_001339537.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
13 REVIEWED NM_001352607.2 NP_001339536.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
14 REVIEWED NM_001352606.2 NP_001339535.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
15 REVIEWED NM_001352605.2 NP_001339534.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
16 REVIEWED NM_001178004.2 NP_001171475.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -
17 REVIEWED NM_001127692.3 NP_001121164.1 NC_000013.11 (100089092..100530434) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1143 reference articles

Variant Information Propionyl-CoA carboxylase subunit alpha (PCCAMutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Propionyl-CoA carboxylase subunit alpha (PCCA)
ClinVar variants:Revealing mutagenic patterns

GO Term of Propionyl-CoA carboxylase subunit alpha (PCCA)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAenablesnucleotide bindingFunction
2Homo sapiensIBAenablespropionyl-CoA carboxylase activityFunction
3Homo sapiensIDAenablespropionyl-CoA carboxylase activityFunction6765947 
4Homo sapiensIEAenablespropionyl-CoA carboxylase activityFunction
5Homo sapiensIMPenablespropionyl-CoA carboxylase activityFunction8434582 
6Homo sapiensIPIenablesprotein bindingFunction20725044 32296183 33961781 
40205054 
7Homo sapiensIEAenablesATP bindingFunction
8Homo sapiensHTPlocated_inmitochondrionComponent34800366 
9Homo sapiensIBAis_active_inmitochondrionComponent
10Homo sapiensIDAlocated_inmitochondrionComponent
11Homo sapiensIDAlocated_inmitochondrial matrixComponent16023992 
12Homo sapiensIEAlocated_inmitochondrial matrixComponent
13Homo sapiensNASlocated_inmitochondrial matrixComponent29033250 
14Homo sapiensTASlocated_inmitochondrial matrixComponent
15Homo sapiensTASlocated_incytosolComponent
16Homo sapiensIEAinvolved_inlipid metabolic processProcess
17Homo sapiensNASinvolved_infatty acid metabolic processProcess29033250 
18Homo sapiensNASinvolved_inbranched-chain amino acid metabolic processProcess29033250 
19Homo sapiensIEAenablesbiotin bindingFunction
20Homo sapiensTASenablesbiotin bindingFunction3460076 
21Homo sapiensIEAinvolved_inlipid catabolic processProcess
22Homo sapiensIEAenablesligase activityFunction
23Homo sapiensIEAenablesligase activity, forming carbon-carbon bondsFunction
24Homo sapiensICinvolved_inshort-chain fatty acid catabolic processProcess6765947 8434582 
25Homo sapiensIPIenablesenzyme bindingFunction19157941 
26Homo sapiensIEAenablesmetal ion bindingFunction
27Homo sapiensIDAinvolved_insuccinyl-CoA biosynthetic processProcess8434582