GenTIGSA Gene Database on Rare Genetic Disorders

Assembly factor for spindle microtubules (ASPM) Associated conditions:  1. Microcephaly 5, primary, autosomal recessive  2. Fetal akinesia deformation sequence 1 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_001206846.2 NP_001193775.1 NC_000001.11 (197084126..197146668, complement) Reference GRCh38.p14 Primary Assembly Q8IZT6
2 REVIEWED NM_018136.5 NP_060606.3 NC_000001.11 (197084126..197146668, complement) Reference GRCh38.p14 Primary Assembly Q8IZT6

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1133 reference articles

Variant Information Assembly factor for spindle microtubules (ASPMMutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Assembly factor for spindle microtubules (ASPM)
ClinVar variants:Revealing mutagenic patterns

GO Term of Assembly factor for spindle microtubules (ASPM)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAinvolved_inneuron migrationProcess
2Homo sapiensIEAinvolved_inpositive regulation of neuroblast proliferationProcess
3Homo sapiensIEAenablescalmodulin bindingFunction
4Homo sapiensIDAlocated_innucleusComponent21044324 
5Homo sapiensIEAlocated_incytoplasmComponent
6Homo sapiensIEAlocated_incentrosomeComponent
7Homo sapiensIMPinvolved_inspindle organizationProcess21044324 
8Homo sapiensIEAinvolved_inspermatogenesisProcess
9Homo sapiensIEAinvolved_inasymmetric cell divisionProcess
10Homo sapiensIEAinvolved_inmale gonad developmentProcess
11Homo sapiensIEAlocated_inapical plasma membraneComponent
12Homo sapiensIEAinvolved_inforebrain neuroblast divisionProcess
13Homo sapiensIEAinvolved_incerebral cortex developmentProcess
14Homo sapiensIEAlocated_inmidbodyComponent
15Homo sapiensIDAlocated_inmicrotubule minus-endComponent21044324 
16Homo sapiensIEAinvolved_innegative regulation of neuron differentiationProcess
17Homo sapiensIEAinvolved_innegative regulation of asymmetric cell divisionProcess
18Homo sapiensIEAinvolved_inoogenesisProcess
19Homo sapiensIEAinvolved_indevelopmental growthProcess
20Homo sapiensIEAinvolved_inregulation of meiotic cell cycleProcess
21Homo sapiensIMPinvolved_inspindle localizationProcess21044324 
22Homo sapiensIEAinvolved_inmaintenance of centrosome locationProcess
23Homo sapiensIEAlocated_inmeiotic spindleComponent
24Homo sapiensIEAinvolved_inpositive regulation of canonical Wnt signaling pathwayProcess
25Homo sapiensIEAinvolved_inmeiotic spindle assemblyProcess
26Homo sapiensIEAinvolved_inneuronal stem cell population maintenanceProcess
27Homo sapiensIDAlocated_inmitotic spindle poleComponent15972725 21044324