GenTIGSA Gene Database on Rare Genetic Disorders

Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL) Associated conditions:  1. Glycogen storage disease type III 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_000028.3 NP_000019.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
2 REVIEWED NM_000642.3 NP_000633.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
3 REVIEWED NM_000643.3 NP_000634.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
4 REVIEWED NM_000644.3 NP_000635.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
5 REVIEWED NM_000646.3 NP_000637.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
6 REVIEWED NM_001425325.1 NP_001412254.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
7 REVIEWED NM_001425326.1 NP_001412255.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
8 REVIEWED NM_001425327.1 NP_001412256.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
9 REVIEWED NM_001425328.1 NP_001412257.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
10 REVIEWED NM_001425329.1 NP_001412258.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -
11 REVIEWED NM_001425332.1 NP_001412261.1 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly -

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 1110 reference articles

Variant Information Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGLMutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL)
ClinVar variants:Revealing mutagenic patterns

GO Term of Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAenablescatalytic activityFunction
2Homo sapiensEXPenables4-alpha-glucanotransferase activityFunction2961257 
3Homo sapiensIBAenables4-alpha-glucanotransferase activityFunction
4Homo sapiensIEAenables4-alpha-glucanotransferase activityFunction
5Homo sapiensEXPenablesamylo-alpha-1,6-glucosidase activityFunction2961257 
6Homo sapiensIBAenablesamylo-alpha-1,6-glucosidase activityFunction
7Homo sapiensIEAenablesamylo-alpha-1,6-glucosidase activityFunction
8Homo sapiensIPIenablesprotein bindingFunction17908927 24837458 
9Homo sapiensTASlocated_inextracellular regionComponent
10Homo sapiensIEAlocated_innucleusComponent
11Homo sapiensIDAlocated_innucleoplasmComponent
12Homo sapiensIDAlocated_incytoplasmComponent17908927 
13Homo sapiensIEAlocated_incytoplasmComponent
14Homo sapiensIDAlocated_incytosolComponent
15Homo sapiensIEAis_active_incytosolComponent
16Homo sapiensTASlocated_incytosolComponent
17Homo sapiensIEAinvolved_incarbohydrate metabolic processProcess
18Homo sapiensIEAinvolved_inglycogen biosynthetic processProcess
19Homo sapiensIBAinvolved_inglycogen catabolic processProcess
20Homo sapiensIEAinvolved_inglycogen catabolic processProcess
21Homo sapiensTASinvolved_inglycogen catabolic processProcess
22Homo sapiensIEAinvolved_inresponse to nutrientProcess
23Homo sapiensIEAinvolved_inresponse to hormoneProcess
24Homo sapiensIEAlocated_ininclusion bodyComponent
25Homo sapiensIEAlocated_insarcoplasmic reticulumComponent
26Homo sapiensIDAlocated_innuclear bodyComponent
27Homo sapiensIEAenablestransferase activityFunction
28Homo sapiensIEAenablesglycosyltransferase activityFunction
29Homo sapiensIEAenableshydrolase activityFunction
30Homo sapiensIEAenableshydrolase activity, acting on glycosyl bondsFunction
31Homo sapiensIEAenablescarbohydrate bindingFunction
32Homo sapiensIEAenablespolysaccharide bindingFunction
33Homo sapiensIEAenablespolyubiquitin modification-dependent protein bindingFunction
34Homo sapiensTASlocated_insecretory granule lumenComponent
35Homo sapiensTASpart_ofisoamylase complexComponent1374391 
36Homo sapiensIEAinvolved_inresponse to glucocorticoidProcess
37Homo sapiensTASlocated_inficolin-1-rich granule lumenComponent