GenTIGSA Gene Database on Rare Genetic Disorders

Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL) Associated conditions:  1. Glycogen storage disease type III 
mRNA Information: Transcript Variants and Protein Isoforms
SNo. Status mRNA accession Protein accession Genomic DNA accession (Chromosome) mRNA location on genomic DNA Assembly UniProtkb ID
1 REVIEWED NM_000028.2 NP_000019.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly P35573
2 REVIEWED NM_000642.3 NP_000633.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly P35573
3 REVIEWED NM_000643.2 NP_000634.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly P35573
4 REVIEWED NM_000644.2 NP_000635.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly P35573
5 REVIEWED NM_000646.2 NP_000637.2 NC_000001.11 (99849257..99924022) Reference GRCh38.p14 Primary Assembly P35573

Transcript variants arise from alternative splicing during gene expression, producing multiple mRNA transcripts from a single gene, each encoding distinct protein isoforms.

PubMed Links for Transcript Variants (Isoforms)
Link 197 reference articles

Variant Information Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGLMutation Visualization Dashboard: Pathogenic variant distribution chart

 

IndiGenomes variants: Exploring and mapping pathogenic variants in gene Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL)
ClinVar variants:Revealing mutagenic patterns

GO Term of Amylo-alpha-1, 6-glucosidase, 4-alpha-glucanotransferase (AGL)
SNo. Reported in speceis Evidence Qualifier GO term Category Pubmed Link
1Homo sapiensIEAenablesglycogen debranching enzyme activityFunction
2Homo sapiensEXPenables4-alpha-glucanotransferase activityFunction2961257 
3Homo sapiensIBAenables4-alpha-glucanotransferase activityFunction21873635 
4Homo sapiensEXPenablesamylo-alpha-1,6-glucosidase activityFunction2961257 
5Homo sapiensIBAenablesamylo-alpha-1,6-glucosidase activityFunction21873635 
6Homo sapiensIPIenablesprotein bindingFunction17908927 24837458 
7Homo sapiensTASlocated_inextracellular regionComponent
8Homo sapiensIEAlocated_innucleusComponent
9Homo sapiensIDAlocated_incytoplasmComponent17908927 
10Homo sapiensTASlocated_incytosolComponent
11Homo sapiensIEAinvolved_inglycogen biosynthetic processProcess
12Homo sapiensIBAinvolved_inglycogen catabolic processProcess21873635 
13Homo sapiensTASinvolved_inglycogen catabolic processProcess
14Homo sapiensIEAinvolved_inresponse to nutrientProcess
15Homo sapiensIEAlocated_ininclusion bodyComponent
16Homo sapiensIEAlocated_insarcoplasmic reticulumComponent
17Homo sapiensIEAenablespolysaccharide bindingFunction
18Homo sapiensIEAenablespolyubiquitin modification-dependent protein bindingFunction
19Homo sapiensTASlocated_insecretory granule lumenComponent
20Homo sapiensTASpart_ofisoamylase complexComponent1374391 
21Homo sapiensIEAinvolved_inresponse to glucocorticoidProcess
22Homo sapiensIEAenablesbeta-maltose 4-alpha-glucanotransferase activityFunction
23Homo sapiensTASlocated_inficolin-1-rich granule lumenComponent